OA01 Multifaceted triggers, diagnostic and management hurdles in hemophagocytic lymphohistiocytosis in a young immunosuppressed adult with systemic juvenile idiopathic arthritis
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Authors
Tripp, Nadia
Coulson, Elizabeth
Issue Date
2024
Type
Presentation
Language
en
Keywords
arthritis , hemophagocytic lymphohistiocytosis , sepsis
Alternative Title
ORAL ABSTRACT PRESENTATIONS.
Abstract
Introduction: We present a case of a 17 year old female with systemic JIA (generally well controlled for a long period on sc Tocilizumab), who presented unwell with fevers, sore throat and significant lymphadenopathy. She was initially treated for tonsillar sepsis in the context of immunosuppression, but clinically deteriorated. Further tests suggested she had a life-threatening condition Haemophagocytic Lymphohistiocytosis (HLH). She received immunosuppressive treatment and her clinical condition improved. Further testing showed EBV was the likely trigger for HLH and treatment was tailored to this, whilst liaising with haematology. She made a good recovery but required nearly a month in hospital.
Description
Citation
‘Oral Abstract Presentations’ (2024) Rheumatology Advances in Practice, 8, pp. i1–i21. Available at: https://research.ebsco.com/linkprocessor/plink?id=9f4a7da1-752f-3cbb-b30e-9bf9207ba9d9 (Accessed: 23 October 2025).
Publisher
License
Journal
Rheumatology Advances in Practice
Volume
Issue
PubMed ID
ISSN
25141775